A Case of Primary Autoimmune Myelofibrosis |
Yeongmin Lim1, Chi Young Park1, Won jung Hong1, Gwangil Kim2, Soyoung Chong1, Doyeun Oh1 |
1Departments of Internal Medicine, School of Medicine, CHA University, Seongnam, Korea 2Departments of Pathology, School of Medicine, CHA University, Seongnam, Korea |
원발성 자가면역 골수섬유증 1예 |
임영민1, 박치영1, 홍원정1, 김광일2, 정소영1, 오도연1 |
1차의과학대학교 내과학교실 2차의과학대학교 병리학교실 |
Correspondence:
Doyeun Oh, Tel: +82-31-780-5217, Fax: +82-31-780-5208, Email: doh@cha.ac.kr |
Received: 29 April 2013 • Revised: 20 May 2013 • Accepted: 1 September 2013 |
|
This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted noncommercial use, distribution, and reproduction in any medium, provided the original work is properly cited. |
Abstract |
Primary autoimmune myelofibrosis, the development of which is not preceded by a well-defined autoimmune disease, has recently been defined as a distinct clinicopathologic syndrome. We report herein a case of a 68-year-old woman who was diagnosed with primary autoimmune myelofibrosis and present a review of the literature. The patient manifested peripheral pancytopenia, was positive for autoantibodies, and developed myelofibrosis with no preceding autoimmune or hematologic disorders. Her condition was dramatically improved after administration of prednisolone. (Korean J Med 2014;86:632-636) |
Key Words:
1. Pullarkat V, Bass RD, Gong JZ, Feinstein DI, Brynes RK.
Primary autoimmune myelofibrosis: definition of a distinct
clinicopathologic syndrome. Am J Hematol 2003;72:8-12.
2. Park SH, Seo YH, Park PH, et al. A case of primary autoimmune
myelofibrosis |
주제어:
원발성 자가면역 골수섬유증; 백적혈구모세포증; 프레드니솔론 |
|