A case of Kartagener's syndrome with acute respiratory failure successfully treated by NPPV

Kyung Hyun Paeck,; Ka Young Lee,; Kyung Hoon Min,; Seoung Ju Park,; Heung Bum Lee,; Yong Chul Lee,; Yang Keun Rhee,

Korean J Med > Volume 73(3); 2007 > Article

Original Article

The Korean Journal of Medicine 2007;73(3):976-980.

A case of Kartagener's syndrome with acute respiratory failure successfully treated by NPPV

Kyung Hyun Paeck, Ka Young Lee, Kyung Hoon Min, Seoung Ju Park, Heung Bum Lee, Yong Chul Lee, Yang Keun Rhee

경희대학교 의과대학 순환기내과학교실

증례 : Kartagener 증후군 환자의 급성호흡부전 - 비침습적 환기치료로 호전된 1예

백경현&#;이가영&#;민경훈&#;박성주&#;이흥범&#;이용철&#;이양근, Ka Young Lee, Kyung Hoon Min, Seoung Ju Park, Heung Bum Lee, Yong Chul Lee, Yang Keun Rhee

Abstract

Kartagener’s syndrome is characterized by the triad of situs inversus, bronchiectasis, and chronic pansinusitis. Pulmonary infections, such as pneumonia or other conditions, aggravate the pulmonary symptoms of Kartagener’s syndrome and lead to the exacerbation of hypoventilation and hypercapnia. These conditions may induce acute respiratory failure (ARF). Noninvasive positive pressure ventilation (NPPV) is known to be safe and well tolerated in patients with Kartagener’s syndrome, and it has assumed a prominent role in the management of ARF. The attractiveness of NPPV is primarily related to its advantages over invasive mechanical ventilation. It is used in patients with ARF due to the exacerbation of chronic obstructive pulmonary disease or cardiogenic pulmonary edema. We report a case of ARF in a patient with Kartagener's syndrome that was successfully treated with NPPV.(Korean J Med 73:S976-S980, 2007)

Key Words: Kartagener's syndrome, Acute respiratory failure, Noninvasive positive pressure ventilation