An intriguing case of primary amyloidosis with cardiac involvement : symptomatic and echocardiographic improvement |
Il-Young Oh, Dae-Won Sohn, Jung-Ju Sir, Yong-Sang, Hong, Sung-Soo Yoon, Young-Bae Park, Yun-Shik Choi |
한양대학교 내과학 교실 |
증례 : Thalidomide 치료 후 호전된 심장 침범을 동반한 원발성 아밀로이드증 1예 |
오일영손대원서정주홍용상윤성수박영배최윤식, Dae-Won Sohn, Jung-Ju Sir, Yong-Sang, Hong, Sung-Soo Yoon, Young-Bae Park, Yun-Shik Choi |
|
|
|
Abstract |
Patients with primary amyloidosis (AL) have poor prognosis with a median survival of one to two years. In patients with symptomatic cardiac involvement, prognosis is even worse with the reported median survival of 6 months. One patient, diagnosed as AL amyloidosis with cardiac involvement, was treated with thalidomide and showed remarkable improvement in functional capacity, cardiac function, and various laboratory parameters without any significant adverse effect and, therefore, we report the case with the review of literatures.(Korean J Med 69:S910-S914, 2005) |
Key Words:
Amyloidosis, Thalidomide |
|