-
Case Report
-
Korean J Med. 2015;88(1):69-73. Published online January 1, 2015.
DOI: https://doi.org/10.3904/kjm.2015.88.1.69
- 우심실부전이 동반된 단독우심실비치밀화증
-
임상혁1, 안지훈2, 오태훈1, 이동현1, 박민우1
-
1순천향대학교 의과대학 순천향대학교 천안병원 내과
2순천향대학교 의과대학 순천향대학교 구미병원 내과
- Isolated Right Ventricular Noncompaction Accompanied by Right Ventricular Failure
-
Sanghyok Lim1, Jihun Ahn2, Taehun O1, Donghyun Lee1, Minwoo Park1
-
1Department of Internal Medicine, Soonchunhyang University Cheonan Hospital, Soonchunhyang University College of Medicine, Cheonan, Korea
2Department of Internal Medicine, Soonchunhyang University Gumi Hospital, Soonchunhyang University College of Medicine, Cheonan, Korea
- Corresponding author: Jihun Ahn ,Tel: +82-54-468-9062, Fax: +82-54-468-3638, Email: jichoona@gmail.com
- Received: January 23, 2014; Revised: May 20, 2014 Accepted: July 29, 2014.
-
- Abstract
- Noncompaction of the ventricular myocardium is a rare congenital cardiomyopathy caused by arrest of normal endomyocardial embryogenesis. Isolated right ventricular noncompaction (IRNC) is an even rarer form of this disease. We report herein on a 68 year-old male diagnosed with IRNC who presented with right-sided heart failure, without involvement of the left ventricle. Diagnosis was achieved with the aid of echocardiography and ventriculography. Medical treatment including prescription of diuretics, a calcium channel blocker, and digitalis, improved both the symptoms and right ventricular function.
Keywords :Right ventricular noncompaction, Echocardiography, Right-sided heart failure
