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Case Report
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Korean J Med. 2015;88(1):114-119. Published online January 1, 2015.
DOI: https://doi.org/10.3904/kjm.2015.88.1.114
- 비후성 뇌수막염과 대동맥주위염으로 발현한 IgG4 연관 질환 1예
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은정수, 권상훈, 이은송, 강영모, 남언정
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경북대학교 의학전문대학원 내과학교실
- A Case of IgG4-Related Disease with Pachymeningitis and Periaortitis
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Jung Su Eun, Sang Hoon Kwon, Eun Song Lee, Young Mo Kang, Eon Jeong Nam
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Department of Internal Medicine, Kyungpook National Universitiy School of Medicine, Daegu, Korea
- Corresponding author: Eon Jeong Nam ,Tel: +82-53-420-5493, Fax: +82-53-426-2046, Email: ejnam@knu.ac.kr
- Received: July 30, 2014; Revised: August 20, 2014 Accepted: September 11, 2014.
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- Abstract
- Immunoglobulin G4 (IgG4)-related disease (RD) is an immune-mediated, systemic fibroinflammatory condition characterized by a lymphoplasmacytic infiltration of IgG4-positive plasma cells, storiform fibrosis, and obliterative phlebitis. IgG4-RD has become recognized with increasing frequency since the turn of the century and may affect almost any organ. IgG4-RD also involves the meninges but, to the best of our knowledge, no case of IgG4-related intracranial pachymeningitis with periaortitis has been reported in Korea to date. Here, we report on a 65 year-old male with IgG4-RD involving the meninges and aorta.
Keywords :Immunoglobulin G4, Meningitis, Periaortitis
