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Case Report
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Korean J Med. 2014;86(6):770-773. Published online June 1, 2014.
DOI: https://doi.org/10.3904/kjm.2014.86.6.770
- 양측성 원발성 부신 침범의 T-림프모구백혈병/림프종 1예
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정철민1, 송서영1, 김선욱1, 이동현1, 정호철1, 이호진1, 류영준2
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1강원대학교 의학전문대학원 강원대학교병원 내과
2강원대학교 의학전문대학원 강원대학교병원 병리과
- A Case of T-Lymphoblastic Lymphoma/Leukemia with Bilateral Primary Adrenal Involvement
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Chul Min Jung1, Seo-Young Song1, Sun Wook Kim1, Dong Hyun Lee1, Hochul Jung1, Ho Jin Lee1, Youngjoon Ryu2
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1Departments of Internal Medicine, Kangwon National University Hospital, Kangwon National University School of Medicine, Chuncheon, Korea
2Departments of Pathology, Kangwon National University Hospital, Kangwon National University School of Medicine, Chuncheon, Korea
- Corresponding author: Seo-Young Song ,Tel: +82-33-258-9211, Fax: +82-33-258-2455, Email: sysong@kangwon.ac.kr
- Received: August 6, 2013; Revised: September 2, 2013 Accepted: October 2, 2013.
- 현재까지 성인에서 보고된 부신의 원발 림프종은 B세포에서 기원하는 경우가 드물게 보고되었다. 저자들은 복통을 주소로 내원한 51세 여자 환자에서 양측 부신의 종괴를 확인하였고 이후 DIC가 동반되는 급격한 임상 경과를 보인 T-림프모구백혈병/림프종을 경험하였기에 문헌고찰과 함께 보고하는 바이다.
߽ɾ :림프모구백혈병/림프종; T-세포; 부신
- Abstract
- T-lymphoblastic leukemia/lymphoma is an aggressive condition with frequent involvement of the mediastinum, occurring most frequently in older children, adolescents, and young adults. The involvement of extranodal sites is less common, and abdominal dissemination is unusual, but when present it primarily involves the liver and spleen. However, primary lymphoma of the adrenal glands is rare. The majority of reported cases presented with a B-cell immunophenotype. Herein, we report the case of a patient with T-lymphoblastic leukemia/lymphoma who presented predominantly with bilateral adrenal masses without lymphadenopathy, and whose clinical course deteriorated rapidly. (Korean J Med 2014;86:770-773)
Keywords :Lymphoblastic, Leukemia-lymphoma, T-cell, Adrenal glands
