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Case Report
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Korean J Med. 2014;86(5):603-607. Published online May 1, 2014.
DOI: https://doi.org/10.3904/kjm.2014.86.5.603
- 바터팽대부에 점막하 종양으로 보인 신경절세포 부신경절종 1예
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양재훈1, 천영국1, 이태윤1, 심찬섭1, 김욱연2
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1건국대학교 의과대학 내과학교실
2건국대학교 의과대학 병리학교실
- A Gangliocytic Paraganglioma Presenting as a Submucosal Tumor in the Ampulla
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Jae Hoon Yang1, Young Koog Cheon1, Tae Yoon Lee1, Chan Sup Shim1, Wook Youn Kim2
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1Departments of Internal Medicine, Konkuk University School of Medicine, Seoul, Korea
2Departments of Pathology, Konkuk University School of Medicine, Seoul, Korea
- Corresponding author: Young Koog Cheon ,Tel: +82-2-2030-7747, Fax: +82-2-2030-7748, Email: 20110235@kuh.ac.kr
- Received: August 26, 2013; Revised: September 24, 2013 Accepted: October 28, 2013.
- 신경절세포 부신경절종은 드물게 발생하는 신경내분비 종양으로 양성 질환으로 간주되어 왔다. 그러나 림프절전이 나 기타 타 장기로의 원격전이가 확인된 예도 보고되고 있 어 반드시 원격전이 가능성을 고려해야 한다. 신경절세포 부 신경절종은 내시경 소견만으로는 진단이 어렵고 결국 조직 학적 진단이 반드시 필요하다. 최근 저자들은 내시경 유두부 절제술 후 2년 동안 재발을 보이지 않는 점막하 종양 형태를 가진 신경절세포 부신경절종 1예를 문헌고찰과 함께 보고하 는 바이다.
߽ɾ :신경절세포 부신경절종; 내시경 점막 절제술
- Abstract
- A gangliocytic paraganglioma (GP) is a rare benign neuroendocrine tumor. However, its origin remains unclear. It is seen most frequently in the second portion of the duodenum. At endoscopy, a GP characteristically appears as a pedunculated nodular submucosal tumor with erosions and surface ulcers. The histological diagnosis is usually made from endoscopic biopsies showing the presence of epithelioid, spindle, and ganglion cells. We experienced a case of GP in a 38-year-old female who was referred because of a possible ampullary tumor. The endoscopic images showed a 1.5-cm, oval ampullary tumor covered with normal mucosa. An endoscopic biopsy showed chronic duodenitis. The tumor was removed by an endoscopic papillectomy. We report a case of duodenal GP that presented as a submucosal tumor that was treated with a papillectomy and review the literature. (Korean J Med 2014;86:603-607)
Keywords :Paraganglioma, Gangliocytic, Endoscopic mucosal resection
