| A case of Asian-variant intravascular large B-cell lymphoma, diagnosed by splenectomy |
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Jee Young Han, Hyeon Gyu Yi, Jin Soo Lee, Suk Jin Choi, Joo Han Lim, Chul Soo Kim, Moon Hee Lee |
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| 비장절제술로 진단된 아시아변종 혈관내대B세포림프종 1예 |
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한지영·이현규·이진수·최석진·임주한·김철수·이문희, Hyeon Gyu Yi, Jin Soo Lee, Suk Jin Choi, Joo Han Lim, Chul Soo Kim, Moon Hee Lee |
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| Abstract |
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Intravascular large B cell lymphoma (IVLBCL) is a rare form of non-Hodgkin’s lymphoma, characterized by systemic proliferation
of neoplastic B cells within blood vessels. The diagnosis is frequently delayed, because of the lack of clues in imaging
studies. The course is usually aggressive and fatal. Asian-variant intravascular large B cell lymphoma (AIVL) shows characteristic
clinical manifestation as hemophagocytic syndrome, associated with bone marrow and hepatosplenic involvement and, rarely, neurological
abnormalities and skin manifestations. We report the case of a 51-year-old female who was considered initially to have fever
of unknown origin with splenic infarction and was confirmed as AIVL by splenectomy involving liver, spleen, and bone marrow,
with hemophagocytic features. (Korean J Med 77:S1309-S1313, 2009) |
| Key Words:
Intravascular large B-cell lymphoma; Splenectomy; Hemophagocytic syndrome; Fever of unknown origin |
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