Recurrent portal and superior mesenteric vein thrombosis in a patient with idiopathic portal hypertension |
Keum Nam Rim, Joo Hyun Sohn, Hyun Soo Kim, Tae Yeob Kim, Chang Soo Eun, Yong Cheol Jeon, Dong Soo Han |
경희대학교 의과대학 순환기내과학교실 |
증례: 특발성 문맥압 항진증 환자에서 반복적인 간문맥과 상장간막정맥 혈전증 |
임금남손주현김현수김태엽은창수전용철한동수, Joo Hyun Sohn, Hyun Soo Kim, Tae Yeob Kim, Chang Soo Eun, Yong Cheol Jeon, Dong Soo Han |
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Abstract |
Idiopathic portal hypertension (IPH) is characterized by portal hypertension and splenomegaly without portal vein obstruction or significant liver disease. Although IPH may occasionally be accompanied by portal vein thrombosis (PVT) and extrahepatic portal vein thrombosis (EHPVT), recurrent PVT and EHPVT are very rare in IPH. Herein, we report the case of a 30-year-old male who developed IPH with recurrent PVT and EHPVT. Eleven years earlier, the patient had undergone splenectomy and endoscopic sclerotherapy due to hypersplenism and esophageal variceal bleeding, respectively. Ten years earlier, the patient had suffered recurrent esophageal variceal bleeding, which was treated via band ligation, and was diagnosed with IPH via portography and liver biopsy. Then, 8 years prior to presentation, the patient complained of acute abdominal pain and was diagnosed with PVT and EHPVT. After a 6-month course of anticoagulation therapy, the PVT and EHPVT resolved completely. However, 8 years later, he complained again of abdominal pain and was diagnosed with recurrent PVT and EHPVT. (Korean J Med 75:337-342, 2008) |
Key Words:
Anticoagulation; Idiopathic portal hypertension; Portal vein thrombosis; Superior mesenteric vein thrombosis. |
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