A case of jejunal primitive neuroectodermal tumor in an adult female |
Ki Hwan Kim, Ji young Rhee, Jae Kyung Lee, Hwa Young Cho, Seock-Ah Im, Kyu Joo Park, Chong Jai Kim |
성균관대학교 의과대학 삼성서울병원 심장혈관센터 순환기내과 |
증례 : 38세 여자의 공장에서 발생한 원시신경외배엽종양 1예 |
김기환.이지영.이재경.조화영.임석아.박규주.김종재, Ji young Rhee, Jae Kyung Lee, Hwa Young Cho, Seock-Ah Im, Kyu Joo Park, Chong Jai Kim |
|
|
|
Abstract |
Primitive neuroectodermal tumor (PNET) is frequent in children and adolescents, but rare in adults. Most of the extraosseous Ewing’s sarcoma or PNET occur in the soft tissues of the extremities, the paravertebral region, and the pelvic cavity. PNET in the gastrointestinal tract is uncommon. We report herein a case of PNET arising from the jejunum in a 38-year-old woman. She presented with anorexia, nausea, vomiting, and weight loss. Abdominal computed tomography revealed a mass in the small bowel with obstruction. She had a small bowel segmental resection, from which PNET was diagnosed. Multi-agent chemotherapy comprised of vincristine, adriamycin, cyclophophamide, ifosfamide, and etoposide (VAC/IE) was administered for 1 year. The treatment was well-tolerated. She remains alive and continues to be disease free 30 months postoperatively. (Korean J Med 75:237-241, 2008)
Key Words: Neuroectodermal Tumors; Chemotherapy; Jejunum |
Key Words:
Neuroectodermal Tumors; Chemotherapy; Jejunum |
|