| A case report of male congenital long QT syndrome presented with aborted sudden cardiac death |
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고려대학교 의과대학 내과학교실 |
| 증례 : 급작한 심장돌연사로 발현된 남자 선천성 QT 간격 연장 증후군 1예 |
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김철현 |
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| Abstract |
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Congenital long QT syndrome is the inherited disease characterized by prolonged QT intervals and polymorphic ventricular tachycardia, particulary in association with emotional or physical stress. It is an heritable ion channel disease caused by a number of mutations in the genes encoding for transmembrane sodium or potassium ion channel proteins. The clinical manifestations vary from sudden cardiac death to being asymtpomic throughout one’s lifetime. In some cases with vague symptoms, a correct diagnosis may be delayed and is frequently misdiagnosed as a seizure disorder. Men are much less prone to the development of cardiac arrest because of shorter QT intervals, as compared with women. In Korea, there has never been reported a sudden cardiac death resulting from congenital long QT syndrome in a male patient.
Here we report a case of a male patient with congenital long QT syndrome that presented with aborted sudden cardiac death.(Korean J Med 72:S200-S205, 2007)
Key Words : Long QT syndrome, Sudden cardiac death, Torsades de Pointes |
| Key Words:
Long QT syndrome, Sudden cardiac death, Torsades de Pointes |
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