Catastrophic Antiphospholipid Syndrome Improved by Anticoagulation Alone |
Yoon Jeong Kim, Seouk Chan Ko, Sung Du Kim, Ho Jun Lee, Myung Jae Yun, Su Hyun Kim, Na Ree Kang |
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항응고 치료만으로 호전된 감염 후 파국성 항인지질 증후군 1예 |
김윤정, 고석찬, 김성두, 이호준, 윤명재, 김수현, 강나리 |
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Abstract |
Catastrophic antiphospholipid syndrome (APS) is an accelerated subtype of APS that results in multiorgan failure. Although catastrophic APS represents about 0.8% of all APS cases, it is usually a life-threatening medical condition that requires high clinical awareness. Catastrophic APS has been managed by various therapies, including anticoagulation, corticosteroids, plasma exchange and IV immunoglobulin, but it still has a high mortality rate. A few cases treated by anticoagulation and steroids have been reported in Korea. In this paper, we report a case of catastrophic APS that improved after anticoagulation therapy alone. Thus, we consider hat our case shows another clinical aspect of catastrophic APS. |
Key Words:
Antiphospholipid syndrome; Pathophysiology; Therapy |
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