A case of essential thrombocythemia in a patient with Behçet’s disease |
Mi Ran Park, Jun Young Im, Jae Shik Jung, Min Jung Jung, Tae Wook Kim, Young Mi Hong, Choong Won Lee |
전남대학교 의과대학 알레르기내과 |
베체트병 환자에서 발생한 특발성 혈소판증가증 1예 |
박미란, 임준영, 정재식, 정민정, 김태욱, 홍영미, 이충원 |
Division of Allergy, Asthma and Clinical Immunology, Department of Internal Medicine, Chonnnam National University Medical School, Gwangju, Korea |
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Abstract |
Behçet’s disease (BD) is a chronic inflammatory disorder characterized by vasculitis of unknown cause and involving multiple
organs. Its pathogenesis includes neutrophil hyperfunction and the overproduction of inflammatory cytokines, including INF‐α. BD
is often accompanied by leukocytosis, but is rarely associated with myeloproliferative disease. Essential thrombocythemia (ET) is a
myeloproliferative disorder characterized by marked thrombocytosis and marrow megakaryocytic hyperplasia. Only one case of
ET associated with incomplete‐type intestinal BD during hydroxyurea treatment has been reported.
Here, we report a case of essential thrombocythemia in 53‐year‐old female with BD who had taken no medication. Based on the
history, physical examination, and routine laboratory and bone marrow examination, we diagnosed her with ET. (Korean J Med
78:776-779, 2010) |
Key Words:
Behçet’s Disease; Thrombocythemia, essential |
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