A case of systemic sclerosis manifested by heart failure associated with a large pericardial effusion |
Dae Rim Park, Jin-Wuk Hur, Ji Young Park, Se Young Kim, Sung Kee Ryu, Yeong Shil Joo |
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증례 : 다량의 심낭삼출을 동반한 심부전으로 발현된 전신성 경화증 1예 |
박대림.허진욱.박지영.김세영.유승기.주영실, Jin-Wuk Hur, Ji Young Park, Se Young Kim, Sung Kee Ryu, Yeong Shil Joo |
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Abstract |
Systemic sclerosis is a connective tissue disease characterized clinically by a variable degree of skin and visceral organ involvement. Patients with symptomatic cardiac involvement, due to systemic sclerosis, have a poor prognosis. Among the cardiac complications, secondary cardiac complications due to systemic or pulmonary hypertension are most common in systemic sclerosis. The primary cardiac involvement includes pericarditis, pericardial effusion, myocardial fibrosis, heart failure, conduction disturbances, and arrhythmias. Necropsy studies report pericardial involvement in between 33 and 72% of cases, while symptoms of pericarditis occur in only 7 to 20% of patients. The pericardial effusion usually manifests after the other clinical and serologic features of scleroderma. We report a case of scleroderma that presented with a large pericardial effusion, which antedated the other clinical and serologic features of scleroderma. (Korean J Med 75:S917- S920, 2008) |
Key Words:
Systemic sclerosis; Pericardial effusion |
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