| A Case of IgG4-Related Disease with Pachymeningitis and Periaortitis |
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Jung Su Eun, Sang Hoon Kwon, Eun Song Lee, Young Mo Kang, Eon Jeong Nam |
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Department of Internal Medicine, Kyungpook National Universitiy School of Medicine, Daegu, Korea |
| 비후성 뇌수막염과 대동맥주위염으로 발현한 IgG4 연관 질환 1예 |
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은정수, 권상훈, 이은송, 강영모, 남언정 |
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경북대학교 의학전문대학원 내과학교실 |
Correspondence:
Eon Jeong Nam, Tel: +82-53-420-5493, Fax: +82-53-426-2046, Email: ejnam@knu.ac.kr
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Received: 30 July 2014 • Revised: 20 August 2014 • Accepted: 11 September 2014 |
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| This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted noncommercial use, distribution, and reproduction in any medium, provided the original work is properly cited. |
| Abstract |
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Immunoglobulin G4 (IgG4)-related disease (RD) is an immune-mediated, systemic fibroinflammatory condition characterized by a lymphoplasmacytic infiltration of IgG4-positive plasma cells, storiform fibrosis, and obliterative phlebitis. IgG4-RD has become recognized with increasing frequency since the turn of the century and may affect almost any organ. IgG4-RD also involves the meninges but, to the best of our knowledge, no case of IgG4-related intracranial pachymeningitis with periaortitis has been reported in Korea to date. Here, we report on a 65 year-old male with IgG4-RD involving the meninges and aorta. |
| Key Words:
Immunoglobulin G4; Meningitis; Periaortitis |
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